Specimen Collection Manual and Test Catalog
C1 ESTERASE INHIBITOR, FUNCTIONAL
Geisinger Epic Procedure Code: LAB1905 Geisinger Epic ID: 14834Serum
1 ml aliquot of serum; minimum 0.2 mL. Please submit a separate frozen aliquot for this test. It may not be combined with any other test requiring a frozen aliquot.
Freeze serum within 1 hour of time drawn. Do not use gel barrier tubes. Do not submit sample in a glass tube. Freeze and ship frozen. Do not thaw.
Centrifuge 10 minutes at 3000 rpm.
Frozen.
Room temperature: Unacceptable. Refrigerated: Unacceptable. Frozen: 1 month at -20°C.
Room temperature and refrigerated specimens are unacceptable. Gel barrier tubes (SST) are unacceptable.
> or = 68% Normal
41-67% Equivocal
< or = 40% Abnormal
Less than 40% of the reference functional activity indicates a likely diagnosis of hereditary angioedema or acquired C1 Inhibitor deficiency.
The CPT codes provided by GML are based on AMA guidelines and are for informational purposes only.
C1 Inhibitor, Functional
Complement C1 EI Panel Functional, C1 Inactivator,C1 Esterase Inhibitor ,, Quest test code 297, C1ESIF
C1 esterase is decreased in angioedema. The inherited form is usually diagnosed in the first two decades of life. The acquired form affects primarily adults with autoimmune or lymphoproliferative disorders. Approximately 15% of patients with hereditary angioedema have a normal concentration of the protein but it is dysfunctional.